Publications

Authors:

Parcesepe, Pietro; Giordano, Guido; Zanella, Caterina; Giuliani, Jacopo; Greco, Filippo; Bonetti, Andrea; Pancione, Massimo; Manfrin, Erminia; Molinari, Enrico; Latiano, Tiziana Pia; D'Andrea, Mario Rosario; Fassan, Matteo; Olivieri, Nunzio; Remo, Andrea

Title:

Colonic Ewing Sarcoma/PNET associated with liver metastases: A systematic review and case report

Year:

2019

Type of item:

Articolo in Rivista

Tipologia ANVUR:

Articolo su rivista

Language:

Inglese

Referee:

No

Name of journal:

Pathology. Research and Practice

ISSN of journal:

0344-0338

N° Volume:

215

Number or Folder:

2

Page numbers:

387-391

Keyword:

Colon; Ewing Sarcoma; Extra osseous sarcoma; Liver metastases; PNET; Rectum

Short description of contents:

Ewing Sarcoma is a highly lethal undifferentiated tumor of bone. ES is a small round cell tumor with etiological and characteristic chromosomal translocations between TET/FET (TLS/FUS, EWSR1, and TAF15) and ETS (E26 transformation-specific) family genes. Generally, therapeutic approach for metastatic Ewing Sarcoma includes both local (surgery and radiotherapy) and systemic (chemotherapy) disease control with an overall cure rate of 20%. For extra-osseous tumors, the most common primary sites of disease are trunk, extremities, head and neck, retroperitoneum. Among other sites, Ewing Sarcoma/PNET may also rarely arise in colon and rectum. Even if colonic Ewing Sarcoma/PNET have been previously reported in 5 cases, none of those reports came from right side of the colon. In this article, we report the first case of right-sided Ewing Sarcoma with synchronous liver metastases completely responding to first line chemotherapy. Furthermore, we provide a systematic qualitative review of the current literature on adult colorectal Ewing Sarcoma using the Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA).

Product ID:

105913

Handle IRIS:

11562/989677

Last Modified:

November 15, 2022

Bibliographic citation:

Parcesepe, Pietro; Giordano, Guido; Zanella, Caterina; Giuliani, Jacopo; Greco, Filippo; Bonetti, Andrea; Pancione, Massimo; Manfrin, Erminia; Molinari, Enrico; Latiano, Tiziana Pia; D'Andrea, Mario Rosario; Fassan, Matteo; Olivieri, Nunzio; Remo, Andrea, Colonic Ewing Sarcoma/PNET associated with liver metastases: A systematic review and case report «Pathology. Research and Practice» , vol. 215 , n. 2 , 2019 , pp. 387-391

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